Paediatric cardiomyopathies: Echocardiographic diagnosis, clinical profile, and demographic characteristics: The experience of a tertiary referral centre for Latin American paediatric cardiology

Víctor M. Huertas-Quiñones, Camilo F. Mestra, Valeria Peña-Trujillo, Sebastián Gallo-Bernal, Mariana Villaveces, Laura C. Alarcón-Forero

Producción científica: Contribución a una revistaArtículo de Investigaciónrevisión exhaustiva

5 Citas (Scopus)

Resumen

Background: Although multiple studies have been conducted in the adult population, there is a vast knowledge gap regarding the epidemiologic characteristics of cardiomyopathies in the paediatric population. This issue is even more crucial when the precarious situation of medical research in Latin America is considered. Given the potential impact that these disorders could
have on Latin American health systems, a comprehensive epidemiologic study regarding the clinical profile and sociodemographic characteristics of these patients will influence the way we approach paediatric cardiomyopathies. Methods: An observational retrospective study was conducted at a tertiary referral centre for Colombian and Latin American paediatric cardiology. We analysed all cases of primary cardiomyopathies in children younger than 18 years of age who presented at our institution between 2010 and 2016. Cases of cardiomyopathies were classified according to World Health Organization guidelines. Results: From a total of 29,533 children who attended our institution during the study period, 89 new cases of primary cardiomyopathies were identified. The median age at diagnosis was 11 years (interquartile
range 4–9). Dilated cardiomyopathy accounted for 57.3% (n = 51) of cases; hypertrophic cardiomyopathy, 12.3% (n = 11); restrictive cardiomyopathy, 8.9% (n = 8); non-compacted cardiomyopathy, 7.8% (n = 7); arrhythmogenic ventricular cardiomyopathy, 6.7% (n = 6); and unspecified cardiomyopathy, 6.7% (n = 6). Heart failure was observed in 53.93% of the patients. The overall mortality was 12.36% (n = 11), which included two of eight patients who underwent cardiac transplantation.
Idioma originalInglés estadounidense
Páginas (desde-hasta)462-467
Número de páginas6
PublicaciónCardiology in the Young
Volumen30
N.º4
DOI
EstadoPublicación electrónica previa a su impresión - feb. 17 2020

Áreas temáticas de ASJC Scopus

  • Pediatría, perinaltología y salud infantil
  • Cardiología y medicina cardiovascular

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